| Overview |
| bs-21094R-Biotin |
| OPA3 Polyclonal Antibody, Biotin Conjugated |
| IHC-P, IHC-F |
| Mouse |
| Human, Dog, Cow, Sheep, Horse |
| Specifications |
| Biotin |
| Rabbit |
| KLH conjugated synthetic peptide derived from human OPA3 |
| Polyclonal |
| #REF! |
| IgG |
| 1ug/ul |
| Purified by Protein A. |
| Aqueous buffered solution containing 0.01M TBS (pH 7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol. |
| Store at -20C for 12 months. |
| Target |
| 80207 |
| Q9H6K4 |
| Cytoplasm |
| FLJ22187; FLJ25932; Iraqi Jewish optic atrophy plus (3 methylglutaconicaciduria type 3); MGA3; MGC75494; OPA 3; OPA3 protein; Optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia); Optic atrophy 3 (Iraqi Jewish 'optic atrophy plus'); Optic atrophy 3; Optic atrophy 3 protein. |
| OPA3 may play some role in mitochondrial processes. Defects in OPA3 are the cause of 3-methylglutaconic aciduria type 3 (MGA3), also known as optic atrophy plus syndrome, and of optic atrophy type 3 (OPA3), also known as autosomal dominant optic atrophy and cataract (ADOAC). |
| Application Dilution |
| IHC-P |
1:200-400 |
| IHC-F |
1:100-500 |