Overview |
bs-0494R-Biotin |
ETFA Polyclonal Antibody, Biotin Conjugated |
ELISA, IHC-P, IHC-F |
Mouse, Xenopus laevis |
Human, Rat, Dog, Cow, Sheep, Pig, Horse, Rabbit |
Specifications |
Biotin |
Rabbit |
KLH conjugated synthetic peptide derived from human ETFA |
184-260/333 |
Polyclonal |
IgG |
1ug/ul |
Purified by Protein A. |
Aqueous buffered solution containing 0.01M TBS (pH 7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
Store at -20°C for 12 months. |
Target |
2108 |
Cytoplasm |
ETF-alpha;Electron transfer flavoprotein subunit alpha;electron-transfer-flavoprotein, alpha polypeptide;mitochondrial;Alpha ETF;Alpha-ETF;Electron transfer flavoprotein alpha polypeptide;Electron transfer flavoprotein alpha subunit;Electron transfer flavoprotein subunit alpha;Electron transfer flavoprotein subunit alpha mitochondrial;Electron transfer flavoprotein subunit alpha, mitochondrial;Electron transferring flavoprotein alpha polypeptide;EMA;ETFA;ETFA_HUMAN;GA2. |
ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]. |
Application Dilution |
ELISA |
1:500-1000 |
IHC-P |
1:200-400 |
IHC-F |
1:100-500 |